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Early follow-up of lung disease in infants with cystic fibrosis using the raised volume rapid thoracic compression technique and computed tomography during quiet breathing

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Gauthier R, Cabon Y, Giroux-Metges MA, Du Boisbaudry C, Reix P, Le Bourgeois M, Chiron R, Molinari N, Saguintaah M, Amsallem F, Matecki S

doi: 10.1002/ppul.23786.

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Minimal change in structural, functional and inflammatory markers of lung disease in newborn screened infants with cystic fibrosis at one year

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Davies G, Thia LP, Stocks J, Bush A, Hoo AF, Wade A, Nguyen TTD, Brody AS, Calder A, Klein NJ, Carr SB, Wallis C, Suri R, Pao CS, Ruiz G, Balfour-Lynn IM, London Cystic Fibrosis Collaboration (LCFC).

doi: 10.1016/j.jcf.2020.01.006.

Initial acquisition and succession of the cystic fibrosis lung microbiome is associated with disease progression in infants and preschool children

PLoS Pathog.

Muhlebach MS, Zorn BT, Esther CR, Hatch JE, Murray CP, Turkovic L, Ranganathan SC, Boucher RC, Stick SM, Wolfgang MC

doi: 10.1371/

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Structural Lung Disease following Allergic Bronchopulmonary Aspergillosis Complicating Paediatric Cystic Fibrosis

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McCashney A, Robinson P

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Horati H, Janssens HM, Margaroli C, Veltman M, Stolarczyk M, Kilgore MB, Chou J, Peng L, Tiddens HAMW, Chandler JD, Tirouvanziam R, Scholte BJ

doi: 10.1016/j.jcf.2020.01.010.

Pulmonary Fibrosis

Respiratory rate in infants with cystic fibrosis throughout the first year of life and association with lung clearance index measured shortly after birth

J Cyst Fibros.

Korten I, Kieninger E, Yammine S, Cangiano G, Nyilas S, Anagnostopoulou P, Singer F, Kuehni CE, Regamey N, Frey U, Casaulta C, Spycher BD, Latzin P; SCILD; BILD study group

doi: 10.1016/j.jcf.2018.07.002.

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Phenotypes of Rapid Cystic Fibrosis Lung Disease Progression during Adolescence and Young Adulthood

Am J Respir Crit Care Med.

Szczesniak RD, Li D, Su W, Brokamp C, Pestian J, Seid M, Clancy JP

doi: 10.1164/rccm.

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First experience in Switzerland in Phe508del homozygous cystic fibrosis patients with end-stage pulmonary disease enrolled in a lumacaftor-ivacaftor therapy trial - preliminary results

Swiss Med Wkly.

Murer C, Huber LC, Kurowski T, Hirt A, Robinson CA, Bürgi U, Benden C

doi: 10.4414/smw.2018.14593.

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Early follow-up of lung disease in infants with cystic fibrosis using the raised volume rapid thoracic compression technique and computed tomography during quiet breathing

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